Only your doctor can address the risk of dying from PH in your particular case.

PH is a serious disease, which can be life-threatening. If left untreated, many PH patients will die of PH.

For example, in patients with certain types of PAH (the most severe type of PH), patients live on average 2-3 years, if left untreated. These patients include:

• Patients with idiopathic PAH (IPAH; previously known as PPH)
• Patients with PAH due to connective tissue disease (such as scleroderma)

Some patients with PAH live for many years, even if left untreated.

• Patients with PAH due to congenital heart disease